You Searched For: Butyl+methacrylate

Catalog Number: (BOSSBS-15484R-A750)

Supplier: Bioss

Description: HIBCH is a 386 amino acid protein belonging to the enoyl-CoA hydratase/isomerase family. Localising to the mitochondria, HIBCH is highly expressed in liver and kidney, with lower levels found in heart, muscle and brain. HIBCH hydrolyses HIBYL-CoA, a saline catabolite, and _-hydroxypropionyl-CoA, an intermediate in the minor pathway involved in the metabolism of proprionate. Existing as two alternatively spliced isoforms, the gene encoding HIBCH maps to human chromosome 2q32.2. Defects to this gene result in HIBCH deficiency (HIBCHD), known alternatively as deficiency of _-hydroxyisobutyryl CoA deacylase or methacrylic aciduria. HIBCHD is characterised by the accumulation of methacrylyl-CoA, a highly reactive compound that undergoes addition reactions with free sulfhydryl groups. Phenotypic symptoms include early deterioration of neurological function, delayed motor skill development and hypotonia.

UOM: 1 * 100 µl

Catalog Number: (BOSSBS-15484R-A488)

Supplier: Bioss

Description: HIBCH is a 386 amino acid protein belonging to the enoyl-CoA hydratase/isomerase family. Localising to the mitochondria, HIBCH is highly expressed in liver and kidney, with lower levels found in heart, muscle and brain. HIBCH hydrolyses HIBYL-CoA, a saline catabolite, and _-hydroxypropionyl-CoA, an intermediate in the minor pathway involved in the metabolism of proprionate. Existing as two alternatively spliced isoforms, the gene encoding HIBCH maps to human chromosome 2q32.2. Defects to this gene result in HIBCH deficiency (HIBCHD), known alternatively as deficiency of _-hydroxyisobutyryl CoA deacylase or methacrylic aciduria. HIBCHD is characterised by the accumulation of methacrylyl-CoA, a highly reactive compound that undergoes addition reactions with free sulfhydryl groups. Phenotypic symptoms include early deterioration of neurological function, delayed motor skill development and hypotonia.

UOM: 1 * 100 µl

Catalog Number: (BOSSBS-15484R-A555)

Supplier: Bioss

Description: HIBCH is a 386 amino acid protein belonging to the enoyl-CoA hydratase/isomerase family. Localising to the mitochondria, HIBCH is highly expressed in liver and kidney, with lower levels found in heart, muscle and brain. HIBCH hydrolyses HIBYL-CoA, a saline catabolite, and _-hydroxypropionyl-CoA, an intermediate in the minor pathway involved in the metabolism of proprionate. Existing as two alternatively spliced isoforms, the gene encoding HIBCH maps to human chromosome 2q32.2. Defects to this gene result in HIBCH deficiency (HIBCHD), known alternatively as deficiency of _-hydroxyisobutyryl CoA deacylase or methacrylic aciduria. HIBCHD is characterised by the accumulation of methacrylyl-CoA, a highly reactive compound that undergoes addition reactions with free sulfhydryl groups. Phenotypic symptoms include early deterioration of neurological function, delayed motor skill development and hypotonia.

UOM: 1 * 100 µl

Catalog Number: (BOSSBS-15484R-A680)

Supplier: Bioss

Description: HIBCH is a 386 amino acid protein belonging to the enoyl-CoA hydratase/isomerase family. Localising to the mitochondria, HIBCH is highly expressed in liver and kidney, with lower levels found in heart, muscle and brain. HIBCH hydrolyses HIBYL-CoA, a saline catabolite, and _-hydroxypropionyl-CoA, an intermediate in the minor pathway involved in the metabolism of proprionate. Existing as two alternatively spliced isoforms, the gene encoding HIBCH maps to human chromosome 2q32.2. Defects to this gene result in HIBCH deficiency (HIBCHD), known alternatively as deficiency of _-hydroxyisobutyryl CoA deacylase or methacrylic aciduria. HIBCHD is characterised by the accumulation of methacrylyl-CoA, a highly reactive compound that undergoes addition reactions with free sulfhydryl groups. Phenotypic symptoms include early deterioration of neurological function, delayed motor skill development and hypotonia.

UOM: 1 * 100 µl

Supplier: SARSTEDT

Description: Cuvettes in poly(methyl methacrylate) (PMMA) or polystyrene (PS).

Supplier: HAMILTON BONADUZ

Description: PRP-X500 is a superficially porous polymeric anion exchange column designed for the separation, purification and isolation of proteins, peptides and DNA/RNA. The methacrylate polymeric coating of the PRP-X500 provides a more hydrophilic surface, preventing hydrophobic interaction sample losses.

Catalog Number: (8.00786.0100)

Supplier: Merck

Description: Butyl nicotinate

UOM: 1 * 100 mL

Catalog Number: (06958-1ML-F)

Supplier: Merck

Description: Butyl acrylate, Supelco®

UOM: 1 * 1 mL

Supplier: Merck

Description: Butyl acetate, EMPLURA®, Supelco®

Catalog Number: (8.14141.0010)

Supplier: Merck

Description: (1-Butyl)triphenylphosphonium chloride for synthesis

UOM: 1 * 10 g

Catalog Number: (8.01553.0250)

Supplier: Merck

Description: Butyl glycidyl ether

UOM: 1 * 250 mL

Supplier: Merck

Description: Butyl acrylate stabilised, Sigma-Aldrich®

Supplier: Merck

Description: Butyl isocyanate for synthesis, Sigma-Aldrich®

Supplier: Merck

Description: N-tert-Butyl-6-chloronicotinamide for synthesis, Sigma-Aldrich®

Supplier: Merck

Description: Butyl vinyl ether stabilised for synthesis, Sigma-Aldrich®

Supplier: Merck

Description: For full details of specification and hazards please see www.vwr.com or the VWR Chemicals catalogues