You Searched For: Sodium+stearyl+fumarate

Catalog Number: (MOLE15604498-1KG)

Supplier: Molekula

Description: Fumaric acid

UOM: 1 * 1 kg

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Catalog Number: (BOSSBS-12515R-A350)

Supplier: Bioss

Description: ASL is a member of the lyase 1 family of proteins and is predominantly expressed in the liver. Localizing to the cytoplasm and existing as a homotetramer, ASL catalyzes the hydrolytic cleavage of argininosuccinic acid (ASA) to fumarate and arginine, an essential step of the urea cycle which is crucial for the detoxification of ammonia. This reaction is also involved in the biosynthesis of arginine. In addition, ASL shares high sequence homology with the avian and reptilian eye lens protein, d-crystallin. Mutations in the gene encoding ASL leads to an accumulation of ASA in body fluids and results in Arginosuc-cinic aciduria (ASAuria), an autosomal recessive disorder that is characterized by hyperammonemia, liver enlargement, convulsions, physical and mental retardation, episodic unconsciousness and dry and brittle hair showing trich-orrhexis nodosa (weak points or nodes in the hair shaft).

UOM: 1 * 100 µl

Catalog Number: (BOSSBS-12515R-HRP)

Supplier: Bioss

Description: ASL is a member of the lyase 1 family of proteins and is predominantly expressed in the liver. Localizing to the cytoplasm and existing as a homotetramer, ASL catalyzes the hydrolytic cleavage of argininosuccinic acid (ASA) to fumarate and arginine, an essential step of the urea cycle which is crucial for the detoxification of ammonia. This reaction is also involved in the biosynthesis of arginine. In addition, ASL shares high sequence homology with the avian and reptilian eye lens protein, d-crystallin. Mutations in the gene encoding ASL leads to an accumulation of ASA in body fluids and results in Arginosuc-cinic aciduria (ASAuria), an autosomal recessive disorder that is characterized by hyperammonemia, liver enlargement, convulsions, physical and mental retardation, episodic unconsciousness and dry and brittle hair showing trich-orrhexis nodosa (weak points or nodes in the hair shaft).

UOM: 1 * 100 µl

Catalog Number: (BOSSBS-12515R-A750)

Supplier: Bioss

Description: ASL is a member of the lyase 1 family of proteins and is predominantly expressed in the liver. Localizing to the cytoplasm and existing as a homotetramer, ASL catalyses the hydrolytic cleavage of argininosuccinic acid (ASA) to fumarate and arginine, an essential step of the urea cycle which is crucial for the detoxification of ammonia. This reaction is also involved in the biosynthesis of arginine. In addition, ASL shares high sequence homology with the avian and reptilian eye lens protein, d-crystallin. Mutations in the gene encoding ASL leads to an accumulation of ASA in body fluids and results in Arginosuc-cinic aciduria (ASAuria), an autosomal recessive disorder that is characterised by hyperammonemia, liver enlargement, convulsions, physical and mental retardation, episodic unconsciousness and dry and brittle hair showing trich-orrhexis nodosa (weak points or nodes in the hair shaft).

UOM: 1 * 100 µl

Catalog Number: (BOSSBS-12515R-A488)

Supplier: Bioss

Description: ASL is a member of the lyase 1 family of proteins and is predominantly expressed in the liver. Localizing to the cytoplasm and existing as a homotetramer, ASL catalyzes the hydrolytic cleavage of argininosuccinic acid (ASA) to fumarate and arginine, an essential step of the urea cycle which is crucial for the detoxification of ammonia. This reaction is also involved in the biosynthesis of arginine. In addition, ASL shares high sequence homology with the avian and reptilian eye lens protein, d-crystallin. Mutations in the gene encoding ASL leads to an accumulation of ASA in body fluids and results in Arginosuc-cinic aciduria (ASAuria), an autosomal recessive disorder that is characterized by hyperammonemia, liver enlargement, convulsions, physical and mental retardation, episodic unconsciousness and dry and brittle hair showing trich-orrhexis nodosa (weak points or nodes in the hair shaft).

UOM: 1 * 100 µl

Supplier: MERCK PRODUCTION CHEMICALS

Description: Fumaric acid NF, SAFC®

Catalog Number: (PROOLGCFOR0394.00)

Supplier: LGC Standards PROMOCHEM

Description: Organic Standard, Tiamulin hydrogen fumarate

UOM: 1 * 10 mg

Catalog Number: (EDQMY0000333)

Supplier: EDQM

Description: Organic Standard, Tiamulin hydrogen fumarate, Pack type: Vial

UOM: 1 * 500 mg

Catalog Number: (PROOMM1329.00)

Supplier: LGC Standards PROMOCHEM

Description: Organic Standard, Tenofovir disoproxil fumarate

UOM: 1 * 100 mg

Catalog Number: (PROOMM0383.12)

Supplier: LGC Standards PROMOCHEM

Description: Organic Standard, 3-ethyl 5-methyl 2-[(2-aminoethoxy)methyl]-4-(2-chlorophenyl)-6-methylpyridine-3,5-dicarboxylate fumarate

UOM: 1 * 100 mg

Catalog Number: (EDQMY0001657)

Supplier: EDQM

Description: Organic Standard, Quetiapine fumarate

UOM: 1 * 50 mg

Catalog Number: (PROOMM0386.12)

Supplier: LGC Standards PROMOCHEM

Description: Organic Standard, 3-Ethyl 5-methyl 2-[(2-aminoethoxy)methyl]-4-(2-chlorophenyl)-6-methylpyridine-3,5-dicarboxylate fumarate

UOM: 1 * 100 mg

Catalog Number: (HONCR1157-10MG)

Supplier: Honeywell Chemicals

Description: High quality inorganic and organic reference materials produced according to ISO 9001.

UOM: 1 * 10 mg

Supplier: Alfa Aesar

Description: Thiabendazole, a metal chelator and helminth-specific fumarate reductase inhibitor, is used primarily as an anthelmintic to control infections by helminth organisms.

Catalog Number: (PRSI91-668)

Supplier: ProSci Inc.

Description: Fumarylacetoacetase belongs to the FAH family. Fumarylacetoacetase is primary expressed in liver and kidney. It exists as a homodimer and catalyses the hydrolysis of 4-fumarylacetoacetate into fumarate and acetoacetate. Defects in Fumarylacetoacetase cause tyrosinemia type 1, which is congenital metabolism defect characterised by elevated levels of tyrosine in the blood and urine, and hepatorenal manifestations. Typical features include renal tubular injury, self-mutilation, hepatic necrosis, episodic weakness, and seizures.

UOM: 1 * 50 µG

Catalog Number: (PRSI29-614)

Supplier: ProSci Inc.

Description: ASL is a member of the lyase 1 family. The protein forms a cytosolic homotetramer and primarily catalyzes the reversible hydrolytic cleavage of argininosuccinate into arginine and fumarate, an essential step in the liver in detoxifying ammonia via the urea cycle. Mutations in its gene result in the autosomal recessive disorder argininosuccinic aciduria, or argininosuccinic acid lyase deficiency.This gene encodes a member of the lyase 1 family. The encoded protein forms a cytosolic homotetramer and primarily catalyzes the reversible hydrolytic cleavage of argininosuccinate into arginine and fumarate, an essential step in the liver in detoxifying ammonia via the urea cycle. Mutations in this gene result in the autosomal recessive disorder argininosuccinic aciduria, or argininosuccinic acid lyase deficiency. A nontranscribed pseudogene is also located on the long arm of chromosome 22. Alternatively spliced transcript variants encoding different isoforms have been described.

UOM: 1 * 50 µG